NUDT16L1

Chr 16

nudix hydrolase 16 like 1

This protein regulates TP53BP1, a key DNA damage response factor, by controlling its recruitment to chromatin during double-strand break repair and also binds U8 snoRNA. The gene is not highly constrained against loss-of-function variants (pLI 0.0001, LOEUF 1.7), and no established human disease associations have been reported in the literature to date.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.73
Clinical SummaryNUDT16L1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.73LOEUF
pLI 0.000
Z-score 0.14
OE 0.94 (0.511.73)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.76Z-score
OE missense 0.80 (0.680.95)
93 obs / 116.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.94 (0.511.73)
00.351.4
Missense OE0.80 (0.680.95)
00.61.4
Synonymous OE1.99
01.21.6
LoF obs/exp: 6 / 6.4Missense obs/exp: 93 / 116.2Syn Z: -5.91
DN
0.6648th %ile
GOF
0.4678th %ile
LOF
0.3067th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NUDT16L1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC