NPPA

Chr 1

natriuretic peptide A

Also known as: ANF, ANP, ATFB6, ATRST2, CDD, CDD-ANF, CDP, PND

The protein encoded by this gene belongs to the natriuretic peptide family. Natriuretic peptides are implicated in the control of extracellular fluid volume and electrolyte homeostasis. This protein is synthesized as a large precursor (containing a signal peptide), which is processed to release a peptide from the N-terminus with similarity to vasoactive peptide, cardiodilatin, and another peptide from the C-terminus with natriuretic-diuretic activity. Mutations in this gene have been associated with atrial fibrillation familial type 6. This gene is located adjacent to another member of the natriuretic family of peptides on chromosome 1. [provided by RefSeq, Oct 2015]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtAtrial standstill 2
UniProtAtrial fibrillation, familial, 6

Clinical highlights

Gene-disease validity (ClinGen)
dilated cardiomyopathy · ARNo Known Disease Relationshipno established gene-disease relationship
2
Active trials
103
Pubs (1 yr)
P/LP submissions
P/LP missense
1.74
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.74LOEUF
pLI 0.001
Z-score 0.19
OE 0.91 (0.471.74)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.27Z-score
OE missense 1.08 (0.921.27)
100 obs / 92.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.91 (0.471.74)
00.351.4
Missense OE?1.08 (0.921.27)
00.61.4
Synonymous OE?1.13
01.21.6
LoF obs/exp: 5 / 5.5Missense obs/exp: 100 / 92.8Syn Z: -0.63

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NPPA · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.