NOTCH2NLC

Chr 1AD

notch 2 N-terminal like C

Also known as: ETM6, NIID, OPDM3

Enables Notch binding activity. Involved in cerebral cortex development and positive regulation of Notch signaling pathway. Located in extracellular region. Implicated in essential tremor 6; neuronal intranuclear inclusion disease; and oculopharyngodistal myopathy 3. [provided by Alliance of Genome Resources, Jul 2025]

OMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Neuronal intranuclear inclusion diseaseMIM #603472
AD
Oculopharyngodistal myopathy 3MIM #619473
AD
Tremor, hereditary essential, 6MIM #618866
AD
4
Active trials
72
Pubs (1 yr)
P/LP submissions
P/LP missense
LOEUF
GOF
Mechanism· predicted
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NOTCH2NLC · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.