NOMO1

Chr 16

NODAL modulator 1

Also known as: Nomo, PM5

NOMO1 encodes a component of the multi-pass translocon complex that mediates insertion of multi-pass membrane proteins into cellular membranes, taking over from the SEC61 complex to facilitate insertion of subsequent transmembrane regions. This gene is not well-established as a cause of human disease, with mutations in the nearby ABCC6 gene rather than NOMO1 being responsible for pseudoxanthoma elasticum. The gene shows minimal constraint against loss-of-function variants, suggesting it may be tolerant to protein-disrupting mutations.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.02
Clinical SummaryNOMO1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
86 unique Pathogenic / Likely Pathogenic· 237 VUS of 364 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.02LOEUF
pLI 0.000
Z-score 1.43
OE 0.77 (0.591.02)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.52Z-score
OE missense 0.93 (0.861.01)
454 obs / 486.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.77 (0.591.02)
00.351.4
Missense OE0.93 (0.861.01)
00.61.4
Synonymous OE1.11
01.21.6
LoF obs/exp: 35 / 45.4Missense obs/exp: 454 / 486.1Syn Z: -1.19

ClinVar Variant Classifications

364 submitted variants in ClinVar

Classification Summary

Pathogenic63
Likely Pathogenic23
VUS237
Likely Benign17
Benign1
63
Pathogenic
23
Likely Pathogenic
237
VUS
17
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
63
0
63
Likely Pathogenic
0
0
23
0
23
VUS
0
168
69
0
237
Likely Benign
0
7
3
7
17
Benign
0
0
0
1
1
Total01751588341

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

NOMO1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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