NOL4

Chr 18

nucleolar protein 4

Also known as: CT125, HRIHFB2255, NOLP

The NOL4 protein is predicted to bind RNA and localize to the nucleolus. This gene is highly constrained against loss-of-function variants (pLI = 1.00, LOEUF = 0.22), suggesting mutations would likely cause severe disease, but no specific disease associations have been established yet. The extreme intolerance to functional variants indicates NOL4 likely plays a critical role in cellular function.

Summary from RefSeq
Research Assistant →
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.22
LOEUF· LoF intol.
LOF
Mechanism· predicted
Clinical SummaryNOL4
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.
Some data sources returned errors (1)

pubtator: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.22LOEUF
pLI 0.999
Z-score 5.02
OE 0.09 (0.040.22)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.27Z-score
OE missense 0.66 (0.600.74)
240 obs / 361.3 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.09 (0.040.22)
00.351.4
Missense OE0.66 (0.600.74)
00.61.4
Synonymous OE1.14
01.21.6
LoF obs/exp: 3 / 35.0Missense obs/exp: 240 / 361.3Syn Z: -1.28
DN
0.3395th %ile
GOF
0.2895th %ile
LOF
0.77top 5%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.22

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NOL4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →