NMNAT2

Chr 1

nicotinamide nucleotide adenylyltransferase 2

Also known as: C1orf15, PNAT2

This gene product belongs to the nicotinamide mononucleotide adenylyltransferase (NMNAT) enzyme family, members of which catalyze an essential step in NAD (NADP) biosynthetic pathway. Unlike the other human family member, which is localized to the nucleus, and is ubiquitously expressed; this enzyme is cytoplasmic, and is predominantly expressed in the brain. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…
LOEUF 0.27
Clinical SummaryNMNAT2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.99). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
2 unique Pathogenic / Likely Pathogenic· 25 VUS of 35 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint?
0.27LOEUF
pLI 0.989
Z-score 3.70
OE 0.06 (0.020.27)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint?
2.10Z-score
OE missense 0.57 (0.490.67)
110 obs / 191.9 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.06 (0.020.27)
00.351.4
Missense OE?0.57 (0.490.67)
00.61.4
Synonymous OE?0.99
01.21.6
LoF obs/exp: 1 / 17.9Missense obs/exp: 110 / 191.9Syn Z: 0.05

ClinVar Variant Classifications

35 submitted variants in ClinVar

Classification Summary

Likely Pathogenic2
VUS25
2
Likely Pathogenic
25
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
0
0
0
Likely Pathogenic
1
1
0
0
2
VUS
0
25
0
0
25
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total1260027

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

28 pathogenic / likely-pathogenic (of 32) ClinVar copy-number / structural variants overlap NMNAT2 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

NMNAT2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →