NIPA1

Chr 15AD

NIPA magnesium transporter 1

Also known as: FSP3, SLC57A1, SPG6

This gene encodes a magnesium transporter that associates with early endosomes and the cell surface in a variety of neuronal and epithelial cells. This protein may play a role in nervous system development and maintenance. Multiple transcript variants encoding different isoforms have been found for this gene. Mutations in this gene have been associated with autosomal dominant spastic paraplegia 6. [provided by RefSeq, Nov 2008]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Spastic paraplegia 6, autosomal dominantMIM #600363
AD
0
Active trials
14
Pubs (1 yr)
P/LP submissions
P/LP missense
1.04
LOEUF
Multiple*
Mechanism· predicted
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.04LOEUF
pLI 0.006
Z-score 1.49
OE 0.49 (0.261.04)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
1.94Z-score
OE missense 0.60 (0.510.70)
110 obs / 184.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.49 (0.261.04)
00.351.4
Missense OE?0.60 (0.510.70)
00.61.4
Synonymous OE?1.18
01.21.6
LoF obs/exp: 5 / 10.1Missense obs/exp: 110 / 184.1Syn Z: -1.32

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NIPA1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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