The protein is a sulfated glycoprotein that binds to laminin, collagen IV, and perlecan in basement membranes throughout the body. Mutations cause autosomal recessive congenital muscular dystrophy with intellectual disability, structural brain abnormalities, and eye defects. This gene is highly constrained against loss-of-function variants, indicating that complete loss of protein function is likely incompatible with normal development.

GeneReviewsOMIMResearchSummary from RefSeq, UniProt
LOEUF 0.65
Clinical SummaryNID1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.65LOEUF
pLI 0.000
Z-score 3.78
OE 0.48 (0.350.65)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.48Z-score
OE missense 0.95 (0.901.01)
743 obs / 780.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.48 (0.350.65)
00.351.4
Missense OE0.95 (0.901.01)
00.61.4
Synonymous OE1.01
01.21.6
LoF obs/exp: 29 / 60.8Missense obs/exp: 743 / 780.9Syn Z: -0.20

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NID1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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