NFATC2IP

Chr 16

nuclear factor of activated T cells 2 interacting protein

Also known as: ESC2, NIP45, RAD60

This protein regulates NFAT-driven transcription of specific cytokine genes including IL4, IL5, and IL13 in T-helper 2 cells by recruiting PRMT1 to promote histone methylation and acetylation. Mutations cause autosomal recessive primary immunodeficiency with defective T-helper cell cytokine production, resulting in recurrent infections and immune dysregulation typically presenting in early childhood. The gene shows tolerance to loss-of-function variants, consistent with the recessive inheritance pattern observed clinically.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.02
Clinical SummaryNFATC2IP
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.02LOEUF
pLI 0.000
Z-score 1.51
OE 0.60 (0.371.02)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.64Z-score
OE missense 0.88 (0.780.99)
190 obs / 216.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.60 (0.371.02)
00.351.4
Missense OE0.88 (0.780.99)
00.61.4
Synonymous OE0.81
01.21.6
LoF obs/exp: 10 / 16.7Missense obs/exp: 190 / 216.5Syn Z: 1.42

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NFATC2IP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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