NET1

Chr 10

neuroepithelial cell transforming 1

Also known as: ARHGEF8, NET1A

This gene is part of the family of Rho guanine nucleotide exchange factors. Members of this family activate Rho proteins by catalyzing the exchange of GDP for GTP. The protein encoded by this gene interacts with RhoA within the cell nucleus and may play a role in repairing DNA damage after ionizing radiation. Pseudogenes of this gene are located on the long arms of chromosomes 1, 7 and 18. Alternative splicing results in multiple transcript variants that encode different protein isoforms. [provided by RefSeq, Jul 2012]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtOrthostatic intolerance
1
Active trials
16
Pubs (1 yr)
P/LP submissions
P/LP missense
0.77
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.77LOEUF
pLI 0.000
Z-score 2.50
OE 0.49 (0.330.77)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.08Z-score
OE missense 0.83 (0.750.92)
275 obs / 330.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.49 (0.330.77)
00.351.4
Missense OE?0.83 (0.750.92)
00.61.4
Synonymous OE?0.97
01.21.6
LoF obs/exp: 14 / 28.3Missense obs/exp: 275 / 330.5Syn Z: 0.30

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NET1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.