NEMP2

Chr 2

nuclear envelope integral membrane protein 2

Also known as: TMEM194B

NEMP2 encodes a protein predicted to localize to the nuclear inner membrane and function at the nuclear envelope. Mutations cause autosomal recessive disorders, though the specific clinical phenotypes associated with NEMP2 variants are not well-established in the current literature. The gene shows minimal constraint against loss-of-function variants, suggesting it may tolerate some degree of functional disruption.

OMIMResearchSummary from RefSeq
DNmechanismLOEUF 0.99
Clinical SummaryNEMP2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.99LOEUF
pLI 0.000
Z-score 1.58
OE 0.63 (0.410.99)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.68Z-score
OE missense 0.67 (0.580.77)
135 obs / 202.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.63 (0.410.99)
00.351.4
Missense OE0.67 (0.580.77)
00.61.4
Synonymous OE0.75
01.21.6
LoF obs/exp: 13 / 20.8Missense obs/exp: 135 / 202.4Syn Z: 1.68
DN
0.6744th %ile
GOF
0.6051th %ile
LOF
0.3551th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NEMP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found