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NEDHLS

Chr 15AR

AAA ATPase AFG2B

Also known as: DFNB119, NEDHLS, SPATA5L1

NEDHLS enables protein binding and preribosome binding activities and is involved in ribosomal large subunit biogenesis. Mutations cause a neurodevelopmental disorder with hearing loss and spasticity, inherited in an autosomal recessive pattern. The disorder affects both the nervous system and auditory function, reflecting the protein's essential role in ribosome assembly.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/NEDHLS?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NEDHLS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

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