NEDHELS

Chr 11AR

DEAF1 transcription factor

Also known as: MRD24, NEDHELS, NUDR, SPN, VSVS, ZMYND5

This zinc finger transcription factor regulates its own promoter and target genes important for embryonic development. Mutations cause a neurodevelopmental disorder with hypotonia, impaired expressive language, and with or without seizures, inherited in an autosomal recessive pattern. Note that while RefSeq mentions autosomal dominant cognitive disability, the established OMIM phenotype follows autosomal recessive inheritance.

Summary from RefSeq, OMIM
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Primary Disease Associations & Inheritance

Neurodevelopmental disorder with hypotonia, impaired expressive language, and with or without seizuresMIM #617171
AR
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
LOEUF
Mechanism
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/NEDHELS?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NEDHELS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found