NCAPH

Chr 2AR

non-SMC condensin I complex subunit H

Also known as: BRRN1, CAP-H, CAPH, MCPH23, NCAPH1

This protein functions as a regulatory subunit of the condensin complex, which converts interphase chromatin into condensed mitotic chromosomes and is essential for accurate chromosome condensation in neural stem cells during early neurogenesis. Mutations cause primary microcephaly 23, a disorder affecting cortical brain development and head size. The condition follows autosomal recessive inheritance.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.571 OMIM phenotype
Clinical SummaryNCAPH
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.57LOEUF
pLI 0.000
Z-score 3.61
OE 0.37 (0.240.57)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.09Z-score
OE missense 0.85 (0.780.93)
353 obs / 415.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.37 (0.240.57)
00.351.4
Missense OE0.85 (0.780.93)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 14 / 38.1Missense obs/exp: 353 / 415.7Syn Z: 1.05

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NCAPH · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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