NBPF10

Chr 1

NBPF member 10

Also known as: AB6, AG1

This gene is a member of the neuroblastoma breakpoint family (NBPF) which consists of dozens of recently duplicated genes primarily located in segmental duplications on human chromosome 1. This gene family has experienced its greatest expansion within the human lineage and has expanded, to a lesser extent, among primates in general. Members of this gene family are characterized by tandemly repeated copies of DUF1220 protein domains. Gene copy number variations in the human chromosomal region 1q21.1, where most DUF1220 domains are located, have been implicated in a number of developmental and neurogenetic diseases such as microcephaly, macrocephaly, autism, schizophrenia, cognitive disability, congenital heart disease, neuroblastoma, and congenital kidney and urinary tract anomalies. Altered expression of some gene family members is associated with several types of cancer. This gene family contains numerous pseudogenes. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Oct 2014]

ResearchGenerating clinical summary…
0
Active trials
2
Pubs (1 yr)
P/LP submissions
P/LP missense
1.99
LOEUF
Multiple*
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.99LOEUF
pLI 0.000
Z-score -6.55
OE 2.01 (1.641.99)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-12.41Z-score
OE missense 2.66 (1.982.00)
1174 obs / 440.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?2.01 (1.641.99)
00.351.4
Missense OE?2.66 (1.982.00)
00.61.4
Synonymous OE?2.06
01.21.6
LoF obs/exp: 99 / 49.3Missense obs/exp: 1174 / 440.9Syn Z: -10.98

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NBPF10 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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