NBEAL1

Chr 2

neurobeachin like 1

Also known as: A530083I02Rik, ALS2CR16, ALS2CR17

The NBEAL1 protein binds to protein kinases and is involved in protein localization within the cytosol and membrane compartments. Mutations cause autosomal recessive developmental delays, intellectual disability, and seizures with onset typically in early childhood. This gene is highly constrained against loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq
LOEUF 0.65
Clinical SummaryNBEAL1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.65LOEUF
pLI 0.000
Z-score 5.07
OE 0.54 (0.450.65)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.88Z-score
OE missense 0.85 (0.810.90)
1068 obs / 1255.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.450.65)
00.351.4
Missense OE0.85 (0.810.90)
00.61.4
Synonymous OE0.89
01.21.6
LoF obs/exp: 77 / 142.3Missense obs/exp: 1068 / 1255.1Syn Z: 1.82

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NBEAL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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