NANOGNB

Chr 12

NANOG neighbor homeobox

This gene encodes a predicted DNA-binding transcription factor that regulates RNA polymerase II-mediated transcription in the nucleus. The gene shows minimal constraint against loss-of-function variants (pLI 0.004, LOEUF 1.12), and no definitive disease associations have been established in pediatric or adult populations. Clinical significance of variants in this gene remains uncertain.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
44
P/LP submissions
0%
P/LP missense
1.12
LOEUF
DN
Mechanism· predicted
Clinical SummaryNANOGNB
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
43 unique Pathogenic / Likely Pathogenic· 35 VUS of 87 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.12LOEUF
pLI 0.004
Z-score 1.32
OE 0.54 (0.281.12)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.23Z-score
OE missense 0.92 (0.761.13)
69 obs / 74.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.281.12)
00.351.4
Missense OE0.92 (0.761.13)
00.61.4
Synonymous OE1.20
01.21.6
LoF obs/exp: 5 / 9.3Missense obs/exp: 69 / 74.7Syn Z: -0.85
DN
0.6549th %ile
GOF
0.4776th %ile
LOF
0.3649th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

87 submitted variants in ClinVar

Classification Summary

Pathogenic41
Likely Pathogenic2
VUS35
Likely Benign3
Benign3
41
Pathogenic
2
Likely Pathogenic
35
VUS
3
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
41
0
41
Likely Pathogenic
0
0
2
0
2
VUS
0
26
9
0
35
Likely Benign
0
2
1
0
3
Benign
0
0
3
0
3
Total02856084

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

NANOGNB · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found