NAA35

Chr 9

N-alpha-acetyltransferase 35, NatC auxiliary subunit

Also known as: EGAP, MAK10, MAK10P, bA379P1.1

The protein functions as an auxiliary component of the N-terminal acetyltransferase C (NatC) complex, which acetylates N-terminal methionine residues to protect proteins from degradation and regulates apoptosis and smooth muscle cell proliferation. Pathogenic variants in NAA35 cause autosomal recessive developmental disorders through loss-of-function mechanisms. The gene is highly intolerant to loss-of-function variants, consistent with its essential cellular role.

OMIMResearchSummary from RefSeq, UniProt, Mechanism
LOFmechanismLOEUF 0.14
Clinical SummaryNAA35
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint
0.14LOEUF
pLI 1.000
Z-score 6.02
OE 0.04 (0.020.14)
Highly constrained

Among the most LoF-intolerant genes (~top 3%)

Missense Constraint
3.66Z-score
OE missense 0.48 (0.430.54)
189 obs / 393.5 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.04 (0.020.14)
00.351.4
Missense OE0.48 (0.430.54)
00.61.4
Synonymous OE1.07
01.21.6
LoF obs/exp: 2 / 46.1Missense obs/exp: 189 / 393.5Syn Z: -0.61
DN
0.2997th %ile
GOF
0.4678th %ile
LOF
0.74top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.14

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

NAA35 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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