N4BP2L1

Chr 13

NEDD4 binding protein 2 like 1

Also known as: CG018

N4BP2L1 encodes a protein that may function in adipocyte differentiation and triglyceride accumulation, though its precise role remains unclear. The gene is highly constrained against loss-of-function variants (pLI = 0.84, LOEUF = 0.45), suggesting that mutations would likely cause developmental or neurological phenotypes, but specific associated diseases have not yet been definitively established in the literature.

OMIMResearchSummary from UniProt
LOEUF 0.45
Clinical SummaryN4BP2L1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.84) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
45 unique Pathogenic / Likely Pathogenic· 24 VUS of 76 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.45LOEUF
pLI 0.845
Z-score 2.72
OE 0.10 (0.030.45)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.33Z-score
OE missense 0.67 (0.560.80)
86 obs / 128.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.10 (0.030.45)
00.351.4
Missense OE0.67 (0.560.80)
00.61.4
Synonymous OE0.91
01.21.6
LoF obs/exp: 1 / 10.5Missense obs/exp: 86 / 128.3Syn Z: 0.47

ClinVar Variant Classifications

76 submitted variants in ClinVar

Classification Summary

Pathogenic45
VUS24
Likely Benign1
45
Pathogenic
24
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
45
0
45
Likely Pathogenic
0
0
0
0
0
VUS
0
19
5
0
24
Likely Benign
0
1
0
0
1
Benign
0
0
0
0
0
Total02050070

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

N4BP2L1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC