MYO9A

Chr 15AR

myosin IXA

Also known as: CMS24

This gene encodes a member of the myosin superfamily. The protein represents an unconventional myosin; it should not be confused with the conventional non-muscle myosin-9 (MYH9). Unconventional myosins contain the basic domains of conventional myosins and are further distinguished from class members by their tail domains. They function as actin-based molecular motors. Mutations in this gene have been associated with Bardet-Biedl Syndrome. [provided by RefSeq, Dec 2011]

Primary Disease Associations & Inheritance

Myasthenic syndrome, congenital, 24, presynapticMIM #618198
AR
0
Active trials
5
Pathogenic / LP
456
ClinVar variants
4
Pubs (1 yr)
Missense Z
LOEUF
Clinical SummaryMYO9A
🧬
Gene-Disease Validity (ClinGen)
arthrogryposis syndrome · ARLimited

Limited evidence — not for standalone diagnostic reporting

📋
ClinVar Variants
5 Pathogenic / Likely Pathogenic· 354 VUS of 456 total submissions
📖
GeneReview available — MYO9A
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

gnomad: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

456 submitted variants in ClinVar

Classification Summary

Pathogenic2
Likely Pathogenic3
VUS354
Likely Benign38
Benign59
2
Pathogenic
3
Likely Pathogenic
354
VUS
38
Likely Benign
59
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
2
0
2
Likely Pathogenic
1
0
2
0
3
VUS
0
348
2
4
354
Likely Benign
0
19
5
14
38
Benign
0
7
51
1
59
Total13746219456

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

MYO9A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Landmark / reviewRecent case evidence