MYO1C

Chr 17

myosin IC

Also known as: MMI-beta, MMIb, MyoIC, NMI, myr2

This gene encodes an unconventional myosin that functions as an actin-based molecular motor with ATPase activity, involved in intracellular vesicle transport, glucose transporter recycling, and serving as a component of the hair cell adaptation-motor complex in inner ear sensory cells. Mutations cause autosomal recessive nonsyndromic hearing loss, typically presenting in childhood. The gene shows high constraint against loss-of-function variants, indicating its critical importance for normal cellular function.

OMIMResearchSummary from RefSeq, UniProt
MultiplemechanismLOEUF 0.68
Clinical SummaryMYO1C
🧬
Gene-Disease Validity (ClinGen)
nonsyndromic genetic hearing loss · ADDisputed

Disputed — evidence questions this relationship

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.68LOEUF
pLI 0.000
Z-score 3.70
OE 0.51 (0.390.68)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
-0.64Z-score
OE missense 1.07 (1.001.14)
703 obs / 657.1 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.51 (0.390.68)
00.351.4
Missense OE1.07 (1.001.14)
00.61.4
Synonymous OE1.28
01.21.6
LoF obs/exp: 34 / 66.6Missense obs/exp: 703 / 657.1Syn Z: -3.63
DN
0.74top 25%
GOF
0.72top 25%
LOF
0.2483th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MYO1C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →