MYO1A

Chr 12

myosin IA

Also known as: BBMI, DFNA48, DIAR15, MIHC, MYHL

This gene encodes a member of the myosin superfamily. The protein represents an unconventional myosin; it should not be confused with the conventional skeletal muscle myosin-1 (MYH1). Unconventional myosins contain the basic domains characteristic of conventional myosins and are further distinguished from class members by their tail domains. They function as actin-based molecular motors. Mutations in this gene have been associated with autosomal dominant deafness. Alternatively spliced variants have been found for this gene. [provided by RefSeq, Dec 2011]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDiarrhea 15, congenital

Clinical highlights

Gene-disease validity (ClinGen)
nonsyndromic genetic hearing loss · ADRefutedevidence has disproved this relationship
0
Active trials
5
Pubs (1 yr)
P/LP submissions
P/LP missense
1.32
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — MYO1A
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.32LOEUF
pLI 0.000
Z-score -0.58
OE 1.08 (0.891.32)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.50Z-score
OE missense 1.06 (0.991.13)
588 obs / 555.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.08 (0.891.32)
00.351.4
Missense OE?1.06 (0.991.13)
00.61.4
Synonymous OE?0.97
01.21.6
LoF obs/exp: 66 / 61.1Missense obs/exp: 588 / 555.2Syn Z: 0.33

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MYO1A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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