MYL1

Chr 2AR

myosin light chain 1

Also known as: CMYO14, CMYP14, MLC-1, MLC1, MLC1/3, MLC1F, MLC3F, MYOFTA

The protein is a non-regulatory myosin light chain required for proper formation and maintenance of myofibers in fast skeletal muscle. Mutations cause autosomal recessive congenital myopathy with skeletal muscle involvement. The gene is not highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismARLOEUF 1.361 OMIM phenotype
Clinical SummaryMYL1
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Gene-Disease Validity (ClinGen)
congenital myopathy · ARLimited

Limited evidence — not for standalone diagnostic reporting

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.36LOEUF
pLI 0.000
Z-score 0.79
OE 0.73 (0.411.36)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.52Z-score
OE missense 0.86 (0.731.02)
95 obs / 110.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.73 (0.411.36)
00.351.4
Missense OE0.86 (0.731.02)
00.61.4
Synonymous OE1.10
01.21.6
LoF obs/exp: 7 / 9.7Missense obs/exp: 95 / 110.5Syn Z: -0.50
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedMYL1-related myopathy, congenital, with fast-twitch (type II) fiber atrophyLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.74top 25%
GOF
0.74top 25%
LOF
0.2775th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MYL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗