MVB12B

Chr 9

multivesicular body subunit 12B

Also known as: C9orf28, FAM125B

The protein is a component of the ESCRT-I complex that sorts ubiquitinated cargo proteins from the plasma membrane into endosomal vesicles and multivesicular bodies. The gene has a relatively low LOEUF score (0.462) suggesting intolerance to loss-of-function variants, but no specific human diseases or inheritance patterns have been established for MVB12B mutations based on the provided information.

Summary from RefSeq, UniProt
0
Active trials
4
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.46
LOEUF
Mechanism
Clinical SummaryMVB12B
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.56) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.46LOEUF
pLI 0.559
Z-score 3.29
OE 0.20 (0.100.46)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.67Z-score
OE missense 0.65 (0.560.76)
119 obs / 182.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.100.46)
00.351.4
Missense OE0.65 (0.560.76)
00.61.4
Synonymous OE1.04
01.21.6
LoF obs/exp: 4 / 19.8Missense obs/exp: 119 / 182.6Syn Z: -0.25

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MVB12B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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