MRXSPF

Chr XX-linked

transcription factor binding to IGHM enhancer 3

Also known as: MRXSPF, RCCP2, RCCX1, TFEA, bHLHe33

This gene encodes a basic helix-loop-helix domain-containing transcription factor that binds MUE3-type E-box sequences in the promoter of genes. The encoded protein promotes the expression of genes downstream of transforming growth factor beta (TGF-beta) signaling. This gene may be involved in chromosomal translocations in renal cell carcinomas and other cancers, resulting in the production of fusion proteins. Translocation partners include PRCC (papillary renal cell carcinoma), NONO (non-POU domain containing, octamer-binding), and ASPSCR1 (alveolar soft part sarcoma chromosome region, candidate 1), among other genes. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2013]

Primary Disease Associations & Inheritance

Intellectual developmental disorder, X-linked syndromic, with pigmentary mosaicism and coarse faciesMIM #301066
X-linked
0
ClinVar variants
0
Pathogenic / LP
pLI score
0
Active trials
Clinical SummaryMRXSPF
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/MRXSPF?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MRXSPF · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

OMIM — Genotype-Phenotype Relationships

1 OMIM entry

Intellectual developmental disorder, X-linked syndromic, with pigmentary mosaicism and coarse facies

MIM #301066

Molecular basis of disorder known

X-linked