MRC2

Chr 17

mannose receptor C-type 2

Also known as: CD280, CLEC13E, ENDO180, UPARAP

The protein functions as an endocytotic lectin receptor that internalizes glycosylated ligands and mediates extracellular matrix remodeling through uptake and degradation of collagen matrices via clathrin-mediated endocytosis. No specific pediatric neurogenetic diseases or inheritance patterns associated with MRC2 mutations are documented in the provided information. The protein may regulate protease activity at the cell surface and participate in extracellular matrix remodeling in cooperation with matrix metalloproteinases.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
21
Pubs (1 yr)
12
P/LP submissions
0%
P/LP missense
0.32
LOEUF· LoF intol.
Mechanism
Clinical SummaryMRC2
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.67) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
12 unique Pathogenic / Likely Pathogenic· 88 VUS of 135 total submissions
Some data sources returned errors (1)

pubtator: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.32LOEUF
pLI 0.675
Z-score 6.77
OE 0.22 (0.150.32)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
2.73Z-score
OE missense 0.74 (0.700.79)
661 obs / 889.8 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.22 (0.150.32)
00.351.4
Missense OE0.74 (0.700.79)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 19 / 87.3Missense obs/exp: 661 / 889.8Syn Z: 1.23

ClinVar Variant Classifications

135 submitted variants in ClinVar

Classification Summary

Pathogenic9
Likely Pathogenic3
VUS88
Likely Benign3
Benign2
9
Pathogenic
3
Likely Pathogenic
88
VUS
3
Likely Benign
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
9
0
9
Likely Pathogenic
0
0
3
0
3
VUS
0
87
1
0
88
Likely Benign
0
2
1
0
3
Benign
0
1
1
0
2
Total090150105

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

MRC2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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