MMD2

Chr 7

monocyte to macrophage differentiation associated 2

Also known as: PAQR10

The protein localizes to the Golgi apparatus and modulates Ras signaling as a member of the PAQR family with seven transmembrane domains. Mutations cause Miyoshi muscular dystrophy 2, an autosomal recessive disorder affecting skeletal muscle. This gene is not highly constrained against loss-of-function variants.

OMIMResearchSummary from RefSeq, OMIM
DNmechanismLOEUF 1.421 OMIM phenotype
Clinical SummaryMMD2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.42LOEUF
pLI 0.000
Z-score 0.41
OE 0.88 (0.561.42)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.12Z-score
OE missense 1.03 (0.901.17)
161 obs / 156.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.88 (0.561.42)
00.351.4
Missense OE1.03 (0.901.17)
00.61.4
Synonymous OE1.16
01.21.6
LoF obs/exp: 12 / 13.6Missense obs/exp: 161 / 156.6Syn Z: -0.98
DN
0.75top 25%
GOF
0.5955th %ile
LOF
0.3163th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MMD2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 2 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC