ML4

AR

Mucolipidosis IV

MCOLN1 encodes TRPML1, a calcium-permeable cation channel that regulates calcium release from lysosomes and late endosomes, which is essential for lysosomal trafficking, autophagy, and cellular metal homeostasis. Mutations cause mucolipidosis IV, a progressive neurodevelopmental disorder with intellectual disability, motor delays, and distinctive ophthalmologic findings that typically manifest in infancy. This condition follows autosomal recessive inheritance.

Summary from OMIM, UniProt
Research Assistant →

Primary Disease Associations & Inheritance

Mucolipidosis IVMIM #252650
AR
UniProtMucolipidosis 4
UniProtCorneal dystrophy, Lisch epithelial
3
Active trials
3
Pubs (1 yr)
0
P/LP submissions
P/LP missense
LOEUF
LOF
Mechanism· G2P
Clinical SummaryML4
💊
Clinical Trials
3 active or recruiting trials — potential therapeutic options may be available
📖
GeneReview available — ML4
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/ML4?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ML4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Literature
Open Research Assistant →