MKRN2OS

Chr 3

MKRN2 opposite strand

Also known as: C3orf83, MKRN2-AS1

This gene encodes a long non-coding RNA antisense to the MKRN2 gene that is involved in regulating gene expression. Mutations cause a neurodevelopmental disorder characterized by intellectual disability, developmental delay, and behavioral abnormalities with onset in early childhood. The condition follows an autosomal dominant inheritance pattern, though the gene shows low constraint against loss-of-function variants.

LOEUF 1.65
Clinical SummaryMKRN2OS
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.65LOEUF
pLI 0.000
Z-score 0.24
OE 0.91 (0.511.65)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.10Z-score
OE missense 0.97 (0.841.14)
117 obs / 120.2 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.91 (0.511.65)
00.351.4
Missense OE0.97 (0.841.14)
00.61.4
Synonymous OE1.20
01.21.6
LoF obs/exp: 7 / 7.7Missense obs/exp: 117 / 120.2Syn Z: -1.09

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MKRN2OS · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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