MINK1

Chr 17

misshapen like kinase 1

Also known as: B55, MAP4K6, MEKKK 6, MINK, YSK2, ZC3

The protein is a serine/threonine kinase that regulates neuronal structure, synaptic density, dendrite complexity, and AMPA receptor trafficking, while also activating JNK and p38 MAPK pathways. Pathogenic variants cause autosomal dominant neurodevelopmental disorder with developmental delay, intellectual disability, and behavioral abnormalities. This gene is highly constrained against loss-of-function variants (pLI ~1.0, LOEUF 0.132), indicating that such variants are likely to be pathogenic.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.13
Clinical SummaryMINK1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint
0.13LOEUF
pLI 1.000
Z-score 7.76
OE 0.06 (0.030.13)
Highly constrained

Among the most LoF-intolerant genes (~top 3%)

Missense Constraint
4.08Z-score
OE missense 0.60 (0.550.64)
483 obs / 810.0 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.06 (0.030.13)
00.351.4
Missense OE0.60 (0.550.64)
00.61.4
Synonymous OE1.09
01.21.6
LoF obs/exp: 5 / 79.8Missense obs/exp: 483 / 810.0Syn Z: -1.25
DN
0.4686th %ile
GOF
0.5465th %ile
LOF
0.72top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.13

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MINK1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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