MED27

Chr 9AR

mediator complex subunit 27

MED27 encodes a component of the Mediator complex that functions as a coactivator bridge between gene-specific regulatory proteins and the RNA polymerase II transcription machinery for nearly all RNA polymerase II-dependent genes. Mutations cause autosomal recessive neurodevelopmental disorder with spasticity, cataracts, and cerebellar hypoplasia. The gene shows low constraint against loss-of-function variants (pLI 0.00002), suggesting tolerance to heterozygous loss.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.021 OMIM phenotype
Clinical SummaryMED27
🧬
Gene-Disease Validity (ClinGen)
neurodevelopmental disorder with spasticity, cataracts, and cerebellar hypoplasia · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

ncbi: Error: NCBI fetch failed: 429 https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esearch.fcgi

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.02LOEUF
pLI 0.000
Z-score 1.52
OE 0.60 (0.371.02)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.26Z-score
OE missense 0.73 (0.640.85)
131 obs / 178.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.60 (0.371.02)
00.351.4
Missense OE0.73 (0.640.85)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 10 / 16.7Missense obs/exp: 131 / 178.5Syn Z: 0.03

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MED27 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →