MED17

Chr 11AR

mediator complex subunit 17

Also known as: CRSP6, CRSP77, DRIP80, SRB4, TRAP80

MED17 encodes a component of the Mediator complex, which functions as a coactivator for RNA polymerase II transcription by bridging gene-specific regulatory proteins to the basal transcription machinery. Mutations cause autosomal recessive microcephaly with postnatal progressive features including seizures and brain atrophy. The gene is highly constrained against loss-of-function variants, indicating its critical importance for normal cellular function.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.781 OMIM phenotype
Clinical SummaryMED17
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.78LOEUF
pLI 0.000
Z-score 2.63
OE 0.54 (0.380.78)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.88Z-score
OE missense 0.87 (0.790.95)
298 obs / 343.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.54 (0.380.78)
00.351.4
Missense OE0.87 (0.790.95)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 20 / 37.3Missense obs/exp: 298 / 343.8Syn Z: 0.60

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MED17 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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