ME2

Chr 18

malic enzyme 2

Also known as: ODS1

This gene encodes a mitochondrial NAD-dependent malic enzyme, a homotetrameric protein, that catalyzes the oxidative decarboxylation of malate to pyruvate. It had previously been weakly linked to a syndrome known as Friedreich ataxia that has since been shown to be the result of mutation in a completely different gene. Certain single-nucleotide polymorphism haplotypes of this gene have been shown to increase the risk for idiopathic generalized epilepsy. Alternatively spliced transcript variants encoding different isoforms found for this gene. [provided by RefSeq, Dec 2009]

ResearchGenerating clinical summary…

Clinical highlights

Gene-disease validity (ClinGen)
epilepsy · ARRefutedevidence has disproved this relationship
0
Active trials
71
Pubs (1 yr)
P/LP submissions
P/LP missense
1.06
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.06LOEUF
pLI 0.000
Z-score 1.26
OE 0.77 (0.571.06)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
0.97Z-score
OE missense 0.85 (0.760.94)
265 obs / 313.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.77 (0.571.06)
00.351.4
Missense OE?0.85 (0.760.94)
00.61.4
Synonymous OE?0.92
01.21.6
LoF obs/exp: 27 / 35.0Missense obs/exp: 265 / 313.3Syn Z: 0.64

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ME2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →