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MDDGC2

Chr 14AR

protein O-mannosyltransferase 2

Also known as: LGMD2N, LGMDR14, MDDGA2, MDDGB2, MDDGC2

The protein is an O-mannosyltransferase that requires interaction with POMT1 for enzymatic function and localizes to the endoplasmic reticulum membrane. Mutations cause Walker-Warburg syndrome and muscular dystrophy-dystroglycanopathy (limb-girdle), type C, 2, affecting both brain development and muscle function. Inheritance is autosomal recessive.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/MDDGC2?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MDDGC2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

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