MDC1

Chr 6

mediator of DNA damage checkpoint 1

Also known as: NFBD1

The protein encoded by this gene contains an N-terminal forkhead domain, two BRCA1 C-terminal (BRCT) motifs and a central domain with 13 repetitions of an approximately 41-amino acid sequence. The encoded protein is required to activate the intra-S phase and G2/M phase cell cycle checkpoints in response to DNA damage. This nuclear protein interacts with phosphorylated histone H2AX near sites of DNA double-strand breaks through its BRCT motifs, and facilitates recruitment of the ATM kinase and meiotic recombination 11 protein complex to DNA damage foci. [provided by RefSeq, Jul 2008]

ResearchGenerating clinical summary…
0
Active trials
36
Pubs (1 yr)
P/LP submissions
P/LP missense
0.54
LOEUF
Mechanism
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.54LOEUF
pLI 0.000
Z-score 4.58
OE 0.39 (0.280.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
1.79Z-score
OE missense 0.85 (0.800.90)
942 obs / 1109.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.39 (0.280.54)
00.351.4
Missense OE?0.85 (0.800.90)
00.61.4
Synonymous OE?0.84
01.21.6
LoF obs/exp: 25 / 64.7Missense obs/exp: 942 / 1109.8Syn Z: 2.55

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MDC1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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