MCM3AP

Chr 21AR

minichromosome maintenance complex component 3 associated protein

Also known as: GANP, MAP80, PNRIID, SAC3

The protein encoded by MCM3AP functions as an acetyltransferase that acetylates histones and MCM3, playing roles in DNA replication and mRNA export to the cytoplasm as part of the TREX-2 complex. Mutations cause autosomal recessive peripheral neuropathy with or without impaired intellectual development. This gene is highly constrained against loss-of-function variants and is expressed in brain and neuronal tissues.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.491 OMIM phenotype
Clinical SummaryMCM3AP
🧬
Gene-Disease Validity (ClinGen)
peripheral neuropathy, autosomal recessive, with or without impaired intellectual development · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.49LOEUF
pLI 0.000
Z-score 5.38
OE 0.36 (0.270.49)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.04Z-score
OE missense 1.00 (0.951.05)
1129 obs / 1132.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.36 (0.270.49)
00.351.4
Missense OE1.00 (0.951.05)
00.61.4
Synonymous OE1.07
01.21.6
LoF obs/exp: 30 / 82.8Missense obs/exp: 1129 / 1132.9Syn Z: -1.19

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MCM3AP · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →