MCAHS1

Chr 18AR

phosphatidylinositol glycan anchor biosynthesis class N

Also known as: GPI-ETI, MCAHS, MCAHS1, MCD4, MDC4, PIG-N

The protein transfers phosphoethanolamine to the first mannose of the GPI anchor in the endoplasmic reticulum, which is essential for anchoring proteins to cell surfaces. Mutations cause multiple congenital anomalies-hypotonia-seizures syndrome 1, a disorder affecting the nervous system and multiple organ systems from birth. Inheritance is autosomal recessive.

Summary from RefSeq, OMIM
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Primary Disease Associations & Inheritance

Multiple congenital anomalies-hypotonia-seizures syndrome 1MIM #614080
AR
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
LOEUF
Mechanism
📖
GeneReview available — MCAHS1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/MCAHS1?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MCAHS1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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