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MC4DN7

Chr 19AR

cytochrome c oxidase subunit 6B1

Also known as: COX6B, COXG, COXVIb1, MC4DN7

This gene encodes subunit VIb of cytochrome c oxidase (complex IV), which catalyzes electron transfer from cytochrome c to oxygen as the terminal enzyme of the mitochondrial respiratory chain. Mutations cause mitochondrial complex IV deficiency, nuclear type 7, presenting as severe infantile encephalomyopathy with autosomal recessive inheritance. The condition affects both brain and muscle systems with onset in infancy.

OMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/MC4DN7?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MC4DN7 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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No publications found for MC4DN7