MASTL

Chr 10

microtubule associated serine/threonine kinase like

Also known as: GREATWALL, GW, GWL, MAST-L, THC2

This gene encodes a microtubule-associated serine/threonine kinase. Mutations at this locus have been associated with autosomal dominant thrombocytopenia, also known as thrombocytopenia-2. Alternatively spliced transcript variants have been described for this locus. [provided by RefSeq, Feb 2010]

OMIMResearchGenerating clinical summary…

Clinical highlights

Gene-disease validity (ClinGen)
thrombocytopenia · ADLimitednot for standalone diagnostic reporting
0
Active trials
18
Pubs (1 yr)
P/LP submissions
P/LP missense
0.95
LOEUF
DN
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.95LOEUF
pLI 0.000
Z-score 1.81
OE 0.68 (0.490.95)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
0.50Z-score
OE missense 0.93 (0.861.01)
428 obs / 458.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.68 (0.490.95)
00.351.4
Missense OE?0.93 (0.861.01)
00.61.4
Synonymous OE?0.87
01.21.6
LoF obs/exp: 25 / 36.9Missense obs/exp: 428 / 458.4Syn Z: 1.37

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MASTL · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →