MAP10

Chr 1

microtubule associated protein 10

Also known as: KIAA1383, MTR120

The protein is a microtubule-associated protein that promotes microtubule stability and participates in spindle midzone organization during cell division. Mutations cause neurodevelopmental disorder with microcephaly, seizures, and brain atrophy, inherited in an autosomal recessive pattern. The gene shows extremely high constraint against loss-of-function variants (pLI ~1), indicating that such variants are likely to be pathogenic when present in the homozygous or compound heterozygous state.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 1.34
Clinical SummaryMAP10
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
38 unique Pathogenic / Likely Pathogenic· 161 VUS of 225 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.34LOEUF
pLI 0.000
Z-score 0.04
OE 0.99 (0.741.34)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-1.32Z-score
OE missense 1.16 (1.081.24)
632 obs / 545.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.99 (0.741.34)
00.351.4
Missense OE1.16 (1.081.24)
00.61.4
Synonymous OE1.27
01.21.6
LoF obs/exp: 31 / 31.3Missense obs/exp: 632 / 545.2Syn Z: -3.12

ClinVar Variant Classifications

225 submitted variants in ClinVar

Classification Summary

Pathogenic37
Likely Pathogenic1
VUS161
Likely Benign23
Benign2
37
Pathogenic
1
Likely Pathogenic
161
VUS
23
Likely Benign
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
37
0
37
Likely Pathogenic
0
0
1
0
1
VUS
0
127
34
0
161
Likely Benign
0
15
7
1
23
Benign
0
2
0
0
2
Total0144791224

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

MAP10 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found