MAN2C1

Chr 15AR

mannosidase alpha class 2C member 1

Also known as: CDDG2, MAN6A8, MANA, MANA1

This gene encodes an alpha-mannosidase that cleaves mannose residues on cytoplasmic free oligosaccharides generated during N-glycoprotein degradation. Biallelic mutations cause congenital disorder of deglycosylation 2, an autosomal recessive condition affecting glycoprotein metabolism. The gene shows low constraint to loss-of-function variation (pLI ~0, LOEUF 1.08), consistent with recessive inheritance where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 1.081 OMIM phenotype
Clinical SummaryMAN2C1
🧬
Gene-Disease Validity (ClinGen)
congenital disorder of deglycosylation 2 · ARModerate

Moderate evidence — consider for supplementary testing

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.08LOEUF
pLI 0.000
Z-score 1.06
OE 0.85 (0.681.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.16Z-score
OE missense 0.98 (0.921.05)
627 obs / 638.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.85 (0.681.08)
00.351.4
Missense OE0.98 (0.921.05)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 49 / 57.7Missense obs/exp: 627 / 638.0Syn Z: 0.18

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MAN2C1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →