MAGOH

Chr 1

mago homolog, exon junction complex subunit

Also known as: MAGOH1, MAGOHA

The protein is a core component of the exon junction complex that is required for pre-mRNA splicing, mRNA export, and nonsense-mediated decay pathways. Mutations cause microcephaly with simplified gyral pattern, intellectual disability, and seizures, following an autosomal recessive inheritance pattern. The gene is highly constrained against loss-of-function variants, indicating intolerance to protein-disrupting mutations.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.49
Clinical SummaryMAGOH
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.80) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.49LOEUF
pLI 0.797
Z-score 2.58
OE 0.10 (0.040.49)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.57Z-score
OE missense 0.19 (0.130.29)
15 obs / 79.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.10 (0.040.49)
00.351.4
Missense OE0.19 (0.130.29)
00.61.4
Synonymous OE0.70
01.21.6
LoF obs/exp: 1 / 9.6Missense obs/exp: 15 / 79.4Syn Z: 1.27

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MAGOH · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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