MAGI1

Chr 3

membrane associated guanylate kinase, WW and PDZ domain containing 1

Also known as: AIP-3, AIP3, BAIAP1, BAP-1, BAP1, MAGI-1, MAGI-1b, Magi1d

MAGI1 encodes a scaffolding protein that assembles multiprotein complexes at cell-cell junctions and couples actin fibers to junctions in endothelial cells. Mutations cause autosomal recessive intellectual disability with seizures and spasticity, typically presenting in early childhood. The gene is highly constrained against loss-of-function variants (LOEUF 0.334), indicating intolerance to protein disruption.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.33
Clinical SummaryMAGI1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.56) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.33LOEUF
pLI 0.560
Z-score 6.16
OE 0.22 (0.150.33)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.36Z-score
OE missense 0.87 (0.820.93)
785 obs / 900.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.22 (0.150.33)
00.351.4
Missense OE0.87 (0.820.93)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 16 / 72.7Missense obs/exp: 785 / 900.1Syn Z: -0.32

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

MAGI1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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