LY6E

Chr 8

lymphocyte antigen 6 family member E

Also known as: RIG-E, RIGE, SCA-2, SCA2, TSA-1

The LY6E protein is a GPI-anchored cell surface protein that regulates T-cell proliferation, differentiation and activation through modulation of T-cell receptor signaling, and also restricts coronavirus entry by interfering with spike protein-mediated membrane fusion. Mutations in LY6E cause autosomal recessive severe combined immunodeficiency with microcephaly, growth retardation, and sensitivity to ionizing radiation. The gene shows moderate tolerance to loss-of-function variation (LOEUF 1.116), and the condition typically presents in early infancy with recurrent infections and developmental delays.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
22
Pubs (1 yr)
58
P/LP submissions
0%
P/LP missense
1.12
LOEUF
Mechanism
Clinical SummaryLY6E
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.24) despite low pLI — interpret in context.
📋
ClinVar Variants
58 unique Pathogenic / Likely Pathogenic· 28 VUS of 105 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.12LOEUF
pLI 0.321
Z-score 1.45
OE 0.24 (0.081.12)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.57Z-score
OE missense 0.82 (0.671.01)
67 obs / 81.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.24 (0.081.12)
00.351.4
Missense OE0.82 (0.671.01)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 1 / 4.2Missense obs/exp: 67 / 81.6Syn Z: -0.16

ClinVar Variant Classifications

105 submitted variants in ClinVar

Classification Summary

Pathogenic54
Likely Pathogenic4
VUS28
Likely Benign2
Benign3
54
Pathogenic
4
Likely Pathogenic
28
VUS
2
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
54
0
54
Likely Pathogenic
0
0
4
0
4
VUS
0
19
9
0
28
Likely Benign
0
2
0
0
2
Benign
0
1
0
2
3
Total02267291

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

LY6E · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →