LRRC40

Chr 1

leucine rich repeat containing 40

Also known as: dJ677H15.1

The LRRC40 protein is predicted to function in intracellular signal transduction and is located in cellular membranes. Mutations in this gene have not been definitively associated with human disease based on the available information. The gene shows very low constraint against loss-of-function variants (pLI near zero, LOEUF 1.35), suggesting tolerance to protein disruption.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
22
P/LP submissions
0%
P/LP missense
1.35
LOEUF
Mechanism
Clinical SummaryLRRC40
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
22 unique Pathogenic / Likely Pathogenic· 66 VUS of 121 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.35LOEUF
pLI 0.000
Z-score -0.01
OE 1.00 (0.751.35)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.18Z-score
OE missense 0.97 (0.881.07)
287 obs / 296.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.00 (0.751.35)
00.351.4
Missense OE0.97 (0.881.07)
00.61.4
Synonymous OE0.90
01.21.6
LoF obs/exp: 31 / 30.9Missense obs/exp: 287 / 296.0Syn Z: 0.84

ClinVar Variant Classifications

121 submitted variants in ClinVar

Classification Summary

Pathogenic22
VUS66
Likely Benign8
22
Pathogenic
66
VUS
8
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
22
0
22
Likely Pathogenic
0
0
0
0
0
VUS
0
62
4
0
66
Likely Benign
0
7
1
0
8
Benign
0
0
0
0
0
Total06927096

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

LRRC40 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found