LRRC23

Chr 12

leucine rich repeat containing 23

Also known as: LRPB7, SPGF92

The protein is essential for sperm motility and male fertility, specifically required for proper assembly of radial spoke structures in sperm flagella. Mutations cause spermatogenic failure 92, inherited in an autosomal recessive pattern. This gene shows low constraint against loss-of-function variants (LOEUF 1.218), consistent with its specialized role in male reproductive function.

ResearchSummary from RefSeq, OMIM, UniProt
DNmechanismLOEUF 1.22
Clinical SummaryLRRC23
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.22LOEUF
pLI 0.000
Z-score 0.87
OE 0.78 (0.511.22)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.25Z-score
OE missense 0.95 (0.841.07)
176 obs / 185.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.78 (0.511.22)
00.351.4
Missense OE0.95 (0.841.07)
00.61.4
Synonymous OE0.94
01.21.6
LoF obs/exp: 14 / 18.0Missense obs/exp: 176 / 185.7Syn Z: 0.41
DN
0.6551th %ile
GOF
0.6053th %ile
LOF
0.3260th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LRRC23 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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