LMAN2L

Chr 2ADAR

lectin, mannose binding 2 like

Also known as: MRD69, MRT52, VIPL

The protein functions as a non-cycling endoplasmic reticulum resident cargo receptor that regulates the export of glycoproteins from the ER to the Golgi apparatus and directs misfolded glycoproteins to the ubiquitin-proteasome pathway for degradation. Mutations cause intellectual developmental disorder with both autosomal dominant and autosomal recessive inheritance patterns reported. The gene shows relatively low constraint against loss-of-function variants (LOEUF 1.295), suggesting some tolerance to functional disruption.

Summary from RefSeq, OMIM, UniProt
Research Assistant →

Primary Disease Associations & Inheritance

?Intellectual developmental disorder, autosomal dominant 69MIM #617863
AD
?Intellectual developmental disorder, autosomal recessive 52MIM #616887
AR
0
Active trials
4
Pubs (1 yr)
36
P/LP submissions
6%
P/LP missense
1.29
LOEUF
Mechanism
Clinical SummaryLMAN2L
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
36 unique Pathogenic / Likely Pathogenic· 92 VUS of 150 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.29LOEUF
pLI 0.000
Z-score 0.53
OE 0.87 (0.601.29)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.19Z-score
OE missense 0.96 (0.861.08)
207 obs / 214.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.87 (0.601.29)
00.351.4
Missense OE0.96 (0.861.08)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 18 / 20.6Missense obs/exp: 207 / 214.8Syn Z: -0.24

ClinVar Variant Classifications

150 submitted variants in ClinVar

Classification Summary

Pathogenic25
Likely Pathogenic11
VUS92
Likely Benign16
Benign1
25
Pathogenic
11
Likely Pathogenic
92
VUS
16
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
1
1
23
0
25
Likely Pathogenic
0
1
10
0
11
VUS
4
50
37
1
92
Likely Benign
0
1
4
11
16
Benign
0
0
1
0
1
Total5537512145

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

LMAN2L · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 3 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC