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LGMDR8

Chr 9AR

tripartite motif containing 32

Also known as: BBS11, HT2A, LGMD2H, LGMDR8, TATIP

This gene encodes a TRIM family protein containing zinc-binding domains (RING and B-box motifs) and a coiled-coil region that localizes to cytoplasmic bodies and the nucleus. Mutations cause limb-girdle muscular dystrophy type 8, a progressive muscle weakness disorder primarily affecting the shoulder and pelvic girdle muscles. The condition follows autosomal recessive inheritance.

GeneReviewsOMIMResearchSummary from RefSeq, OMIM
AR1 OMIM phenotype
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GeneReview available — LGMDR8
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/LGMDR8?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LGMDR8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found