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LGMDR12

Chr 11AR

anoctamin 5

Also known as: GDD1, LGMD2L, LGMDR12, TMEM16E

This gene encodes a calcium-activated chloride channel belonging to the anoctamin family of transmembrane proteins. Mutations cause gnathodiaphyseal dysplasia, a rare skeletal disorder affecting jaw and long bone development with autosomal dominant inheritance. The condition primarily involves the musculoskeletal system with characteristic bone fragility and distinctive radiographic features.

OMIMResearchSummary from RefSeq
AR1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/LGMDR12?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LGMDR12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found