LEPID

Chr 16AR

lysyl-tRNA synthetase 1

Also known as: CMTRIB, DEAPLE, DFNB89, KARS, KARS2, KRS, LEPID

Lysyl-tRNA synthetase is a cytoplasmic enzyme that charges tRNAs with lysine during protein synthesis. Mutations cause autosomal recessive progressive infantile-onset leukoencephalopathy with or without deafness, affecting the white matter of the brain and potentially hearing from early infancy.

Summary from RefSeq, OMIM
Research Assistant →

Primary Disease Associations & Inheritance

Leukoencephalopathy, progressive, infantile-onset, with or without deafnessMIM #619147
AR
0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
LOEUF
Mechanism
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/LEPID?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

LEPID · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →